Background: Intestinal-type adenocarcinoma of tongue is a rare entity, accounting for 2% of all the tongue malignancies. Till now, eight cases of primary intestinal adenocarcinoma have been reported. Case Report: A 65 years old male presented with a progressively increasing ulcero-proliferative mass of left lateral tongue since last six months with left cervical lymphadenopathy. The patient underwent thorough panendoscopy, radiological and histopathological evaluation. CK7, CK20 and Ki-67 markers were used to confirm the diagnosis. The patient was started on chemotherapy and was planned for radiotherapy because of the advanced stage of the disease. Conclusion: Primary intestinal-type adenocarcinoma of the tongue is rare and needs to be distinguished from metastatic intestinal adenocarcinoma.