Background: Hepatoblastoma is the most common primary liver tumor in children, although it is a rare malignancy. The diagnosis of embryonal epithelial type hepatoblastoma can be challenging due to its clinic-radiological and histopathological similarity to other childhood small round cell tumors, such as pancreatoblastoma. Case Report: We present the case of an eight-year-old boy who was initially diagnosed with a pancreatic tumor based on imaging. However, a biopsy revealed a small round cell tumor that was eventually confirmed as hepatoblastoma with metastases to the pancreas through immunohistochemistry. Conclusion: Hepatoblastoma can be difficult to diagnose due to its resemblance to other small round cell tumors in children, such as pancreatoblastoma.