Verrucous epidermal nevi are characterized by localized or diffuse, brown or gray-brown verrucous papules which may coalesce to form well-demarcated papillomatous plaques. Various lesions like squamous cell carcinoma, basal cell carcinoma, may arise on epidermal nevus but association with vascular lesion is rare except in epidermal nevus syndromes and proteus syndrome. We report a case of adult onset epidermal verrucous nevus associated with clinical and histopathological features of angiokeratoma.