Congenital hyporhinia, also known as partial arhinia, is a very rare congenital abnormality of nasal embryogenesis with unknown aetiology. It is commonly associated with other craniofacial anomalies.  A one day old neonate presented to our facility with hypoplastic nasal pyramid, hypertelorism, microcephaly, microphthalmia, micrognathia and cleft palate. A case of congenital hyporhinia with associated anomalies in tropics is presented.