Mucormycosis is an opportunistic fungal infection that rarely occurs in immunocompetent individuals. Mucormycosis refers to a serious fungal infection caused by fungi of the order Mucorales. The common clinical presentations of mucormycosis are rhinocerebral, cutaneous, pulmonary, gastrointestinal and disseminated forms. Clinically, most patients with isolated renal mucormycosis present with fever, flank pain, tenderness, hematuria or pyuria. Histopathologic evidence of fungal invasion of the tissues is diagnostic. Early institution of amphotericin-B, combined with nephrectomy offers the best chance for cure. Isolated renal mucormycosis has been seldom reported and is even rarer in children. We present an unusual case of renal mucormycosis in a pediatric patient with no known predisposing factors.