Abstract
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Apert syndrome is a rare genetic disorder characterised by craniofacial and limb abnormalities. These patients have to undergo multiple surgeries. One of these is cranial vault repair which is done for craniofacial anomalies. These cases pose a challenge to the anaesthesiologists not only because of a difficult airway but also problems like bronchospasm, increased secretion and even a difficulty in securing intravenous access. We present case report of a patient who had undergone cranial vault repair and subsequently developed CSF rhinorrhea and was planned for endonasal correction of skull base defect. Mask ventilation was difficult but intubation was relatively easy. The patient was operated in supine position with 15 degree head up position under hypotensive conditions to minimise bleeding and keep ICP under control. The intraoperative period was uneventful. Patient recovered completely from anaesthesia and was shifted to ICU. |
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Keywords :
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Hypertelorism, Macroglossia, Acrocephalosyndactylia, Airway Obstruction, Intubation.
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