Mucocele of appendix is a rare entity characterized by cystic dilation of the appendix due to intraluminal accumulation of mucoid substance resulting from chronic obstruction of appendix orifice due to any inflammatory or neoplastic cause. Pre-operative diagnosis is obligatory to differentiate it from cyst adenocarcinoma. We report a case of giant mucocele which presented as asymptomatic abdominal lump, with brief review of literature regarding its clinical, diagnostic and characteristics.