Takayasu’s arteritis is an inflammatory disease often affecting the ascending aorta and aortic arch, causing obstruction of the aorta and its major arteries. The disease commonly presents in the 2nd or 3rd decade of life, often with a delayed diagnosis. The disease is progressive and there is no definitive therapy. Glucocorticoids and immunosuppressive agents have been reported to be effective in some patients during the active phase. We report a case of Takayasu arteritis who responded well to glucocorticoids and methotrexate.