We describe a rare case of metastasis of Merkel cell carcinoma (MCC) to the jejunum. The patient was a 79-year-old man with a chief complaint of dizziness and palpitation. He sought medical attention 3 days after the dizziness and palpitation had manifested and was admitted to our hospital. His medical history included MCC, prostate carcinoma, abdominal aortic aneurysm, and stroke. We performed an enteroscopic examination and found a neoplastic lesion in the upper jejunum. Evidence of bleeding led us to perform emergency laparoscopic surgery. Pathologic examination revealed small round cells forming a nodule, and immunostaining for epithelial marker CK20 and neuroendocrine marker synaptophysin were positive. The final diagnosis based on histopathologic examination of the resected jejunal tumor was metastatic MCC. Such metastasis is indeed rare, and we consider our patient’s tumor in light of the literature.