Background: Kikuchi-Fujimoto disease (KFD) also known as histiocytic necrotizing lymphadenitis is a rare and self-limiting cause of fever with lymphadenitis. It usually affects females of the reproductive age group with a predominant involvement of cervical lymph nodes. Case Report: We report a case of young boy with Kikuchi-Fujimoto disease who presented with prolonged fever and painless cervical lymphadenopathy. Conclusion: Due to numerous causes of lymphadenopathy, patients are likely to be misdiagnosed with another disease. A high clinical suspicion with histopathological confirmation is essential for early and accurate diagnosis of KFD, which is usually a self-limited condition.