Background: Composite pheochromocytoma (CP) is a rare tumor characterized by co-existence of pheochromocytoma or paraganglioma with other neurogenic tumors. It constitutes less than 3% of all adrenal gland neoplasms and sympatho-adrenal pheochromocytomas. Case Report: We report a rare case of non-functional composite pheochromocytoma-ganglioneuroma in a young girl who presented with abdominal pain and distension and normal urinary metanephrine levels. Conclusion: Histopathological features of CP with a review of relevant literature will be discussed.