About the Journal | Editorial Board | Instructions to Contributors | Submission & Review | Advertise with Us | Subscribe to E- Alerts
Sitemap | Feedback
Advanced search
Journal of Case Reports
Biliary Atresia with Rare Collection of Congenital Anomalies
RMTM Gunawardena1, PAYP Weerawardhana2, AK Lamahewage3
1National Institute for Nephrology, Dialysis and Transplant, Maligawaththa, Sri Lanka; 2Base Hospital, Warakapola, Sri Lanka; 3Lady Ridgeway Hospital for Children, Colombo 10, Sri Lanka.
Corresponding Author:
Dr. RMTM Gunawardena
Email: thilinamg@gmail.com
Received: 03-JAN-2019 Accepted: 24-MAY-2019 Published Online: 05-JUN-2019
DOI: http://dx.doi.org/10.17659/01.2019.0030
Background: Biliary atresia (BA), characterized by progressive inflammatory destruction of the extra-hepatic biliary tree is one differential diagnosis for jaundice in the newborn. It is a diagnosis which should not be missed, as early surgical intervention is associated with better outcome. In upto 37% cases, this condition can be associated with other congenital anomalies. Case Report: A 2 month old baby girl diagnosed with biliary atresia was found to have a rare collection of coexisting anomalies such as dextrocardia, azygos continuation of the inferior vena cava, multiple spleens, central liver, right sided stomach and pre-duodenal portal vein. The baby underwent porto-enterostomy but she progressed to chronic liver failure. Conclusion: The associated anomalies with BA should be actively looked for in a child diagnosed with this condition, as they will affect the prognosis and the treatment approach. 
Keywords : Biliary Atresia, End Stage Liver Disease, Enterostomy, Infant, Jaundice, Portal Vein.
Article Options
Search PubMed for
Search Google Scholar for
Article Statistics
Bookmark and Share