Background: Ventricular tachycardia may be a solitary episode, complication of a structural heart disease or unusually, the manifestation of a serious electrolyte abnormality. Case Report: We present the rare case of a 13-year-old boy who presented with sudden onset ventricular tachycardia that was precipitated by severe hypokalemia. Subsequently, the associated hypertension and metabolic alkalosis prompted a search for an underlying endocrine abnormality. After investigations, the patient was diagnosed as a case of Conn’s syndrome due to a functional adrenal adenoma- a rare diagnosis. Conclusion: The initial presentation of hyperaldosteronism in a child as ventricular tachycardia is extremely rare.