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Journal of Case Reports
Unicuspid Acommissural Aortic Valve with Supra-aortic Membrane: An Extremely Rare Congenital Anomaly
Santosh Kumar Sinha
LPS Institute of Cardiology. G.S.V.M. Medical College Kanpur-208002, Uttar Pradesh, India.
Corresponding Author:
Dr Santosh Kumar Sinha
Email: fionasan@rediffmail.com
Received: 10-MAY-2020 Accepted: 03-SEP-2020 Published Online: 15-JUN-2021
DOI: http://dx.doi.org/10.17659/01.2021.0033
Background: Unicommissural aortic valve (UAV) is diagnosed by means of echocardiography during systole, because absence of cusp separation reveals eccentric “teardrop” opening. Case Report: A 4-month infant was refereed for evaluation of murmur at aortic area by his pediatrician. On examination, peripheral pulses were weak with diminished and delayed carotid upstroke. Transrthoracic echocardiography revealed unicuspid, unicommissural aortic valve (UAV) with moderate aortic stenosis. There was a supra-aortic membrane without any aortic leak. Conclusion: The importance of its early diagnosis lies in its risk of sudden cardiac death which can be mitigated and other associated congenital anomalies can also be corrected. 
Keywords : Aortic Valve Stenosis, Echocardiography, Heart Valve Diseases, Unicuspid Aortic Valve.
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