Background: Granulomatosis with polyangitis (GPA) is a distinct clinicopathological entity characterized by granulamatous vasculitis of upper and lower respiratory tract together with glomerulonephritis. Case Report: We present a case of GPA who presented with fever and skin rash on fifth day of fever. Skin biopsy revealed leucocytoclastic vasculitis and on further evaluation, he was found to be anti-neutrophil cytoplasmic antibody (ANCA) positive and renal biopsy was suggestive of ANCA associated vasculitis. Conclusion: It is important to be familiar with cutaneous manifestations of vasculitis as early diagnosis and prompt management is key to manage systemic vasculitic disorders.