Background: Etiologies of iso-sexual precocious puberty are numerous. Among common causes for precocious puberty, hormone secreting testicular tumors are important. Leydig cell tumor is a sex cord stromal tumor of the testis. This usually presents with precocious puberty in pre-adolescent boys. Case Report: Our patient is a three year old boy who presented to his pediatrician with one year history of iso-sexual precocious puberty. Later, a right testicular mass was detected. He underwent an inguinal orchidectomy. Conclusion: Hormone secreting testicular tumors should be always be high in differential diagnosis in boys who present with precocious puberty and testicular enlargement.